Orphanet: Syndrome congenital d hamartome hypothalamique. Request PDF on ResearchGate | On Jul 1, , J. Mounach and others published Puberté précoce liée à un hamartome hypothalamique. Request PDF on ResearchGate | On May 1, , N. Ech-Cherif El Kettani and others published Hamartome hypothalamique révélant des crises gélastiques.

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Endoscopic Treatment of Hypothalamic Hamartomas

Careful planning and a stepwise approach with the advanced surgical technique will make it possible 24 However, disconnection from the brain for controlling intractable epilepsy would be always feasible regardless of HH size.

Complications Transient short-term memory loss, weight gain, thalamic infarction hjpothalamique memory loss, and hemiparesis have been reported as early complications. Personal information regarding our website’s visitors, including their identity, is confidential.

Surgical indications are intractable GS, neurobehavioral deterioration, and the absence of a cortical lesion on MRI. Consequently, complete disconnection is considered to be more important than resection.

But even though HHs attach to the bilateral hypothalamus, unilateral disconnection is usually enough. Access to the text HTML. Report of four cases.

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Endoscopic Treatment of Hypothalamic Hamartomas

Disconnection of HHs from the hypothalamus with a monopolar coagulator. Because these patients are mostly clinically and socially impaired, pursuing resection or disconnection would be more beneficial for these patients As the nearby vicinity of HHs consists of very critical structures, the utmost effort should be paid hypothalamiqeu reduce collateral damage.

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Ouhabi aA. Slit-like lateral ventricle and giant HHs within a 6-mm space of the third ventricle are no longer limitations in endoscopic disconnection Please review our privacy policy. Epileptic network of hypothalamic hamartoma: Top of the page – Article Outline.

Journal page Archives Contents list. Complete removal of larger or giant HHs is very difficult or nearly impossible with acceptable morbidity. Surgical approaches to hypothalamic hamartomas.

Alternatively, endoscopic surgery, gamma knife surgery, and stereotactic radiofrequency thermo-coagulation have been introduced and presented good outcomes with fewer complications. This activating network results in epileptic discharges through the premotor and frontal opercular areas voluntary systemwhich are located on the same side of the broader attachment Under direct visualization, the hamartoma can be coagulated by a monopolar electric coagulator or hypothalamque by microforceps Fig.


Therefore, concomitant scalp EEG and depth electrode recording inside HHs may be very useful in disconnecting this lesion from intractable epilepsy. Most epileptiform discharges arise from the broad attachment side 31 Hypothalamic hamartoma HH is a benign indolent lesion despite the presentation of refractory epilepsy.

Therefore, one stage operation or single modality of treatment will lose their effectiveness in managing HHs Intrinsic epileptogenesis of hypothalamic hamartomas in gelastic epilepsy. Since the hypothalamic area is critical itself, even though we must achieve a good seizure outcome, we should avoid critical complications.

From hypothalamic hamartoma to cortex: J Neurol Neurosurg Psychiatry. Transendoscopic intraoperative recording of gelastic seizures from a hypothalamic hamartoma.

You can move this window by clicking on the headline. Endoscopic surgery for hypothalamic hamartomas causing medically refractory gelastic epilepsy. The presence of these neurons constitute relevant evidence for ictogenesis of HH 3918 Neurol Med Chir Tokyo hypothalajique